Despite approximately 50 years of progress in the management of com plex congenital heart disease, hypoplastic left heart syndrome (HLHS) has been one of the last cardiac malformations to yield to effective surgical treat ment. The surgical therapies for hypoplastic left heart syndrome have evolved by two quite disparate routes. One approach has been the staged reconstruc tion operations utilizing an initial operation pioneered by many but developed by Dr. William Norwood and subsequently modified by many other investigators. The first stage reconstruction operation has been refined and standardized such that the majority of infants now proceed to second and third stage reconstruc tive operations culminating in a Pontan Kreutzer single ventricle physiology. An alternative surgical approach has been the development of neonatal and infant heart transplantation for HLHS. This approach also has had a signifi cant impact on the treatment of HLHS and other cardiac malformations and has been associated with good intermediate term results. Both of the thera peutic approaches devised for treatment of hypoplastic left heart syndrome have been effective and the outcomes are continuing to improve with each.

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The extensive experience with over 1,000 consecutive cases of HLHS treated at The Children's Hospital of Philadelphia forms the basis of knowledge for this book. Hypoplastic Left Heart Syndrome is a complete compendium of the "state-of-the-art" on the subject of HLHS and related conditions. The spectrum of topics covered include: genetics and prenatal evaluation, diagnostic assessment, pre- and post-operative management, latest developments in surgical strategies, as well as short and intermediate term outcomes. Sections on quality of life issues such as neurological status, feeding, and late complications are also included. Unique chapters on the impact of congenital heart disease on health care economics, concerns of the pediatrician caring for these patients, and a poignant chapter offering thoughts from a patient and families with HLHS round out the book. Hypoplastic Left Heart Syndrome is a single source, complete text.

Inhalt
1 Epidemiology and Genetics.- 2 Fetal Development and Prenatal Evaluation.- 3 Delivery and Obstetrical Issues.- 4 Echocardiographic Imaging.- 5 Pre-Operative Management.- 6 Stage I Reconstruction.- 7 Stage I Postoperative Management.- 8 The Bidirectional Cavopulmonary Shunt.- 9 The Fontan Operation and Modifications.- 10 Anesthetic Management for HLHS.- 11 Cardiac Catheterization.- 12 Nursing Care.- 13 Infant Heart Transplantation.- 14 Neurological Issues.- 15 Feeding Issues and Somatic Growth.- 16 Cardiac Structure and Function.- 17 Arrhythmias After Surgery.- 18 Exercise Physiology and Capacity.- 19 Complications After the Fontan.- 20 Decision Analysis Strategies.- 21 What the Pediatrician Needs to Know.- 22 The Personal Perspective.- 23 Financial Implications.- Epilogue.