This book addresses current topics concerning Landau-Kleffner Syndrome (LKS) and related central auditory disorders from the perspectives of epidemiology, diagnosis, genetics and clinical treatment.LKS is a rare childhood neurological disorder and manifests auditory agnosia as the central auditory verbal dysfunction. In many cases, LKS patients also suffer from epileptic seizures. The book is divided into two parts, the first of which outlines LKS from its historical background to clinical treatment. In turn, the second part examines current topics involving related central auditory disorders, for purposes of comparing them with LKS. The book offers a valuable resource for many specialists, such as pediatric neurologists, neuropsychologists, audiologists and epileptologists, with an interest in this field.

Autorentext

Dr. Makiko Kaga

Department of Child Neurology, Tokyo Metropolitan Medical Center East for Children/Adults with Developmental Disabilities

Dr. Kimitaka Kaga

National Institute of Sensory Organs, National Tokyo Medical Center

Inhalt

1. Introduction.- Part I. Landau-Kleffner syndrome (LKS).- 2. History of LKS and epidemiology.- 3. Diagnostic Paradigms.- 4. Etiology and Genetics.- 5. Treatment and Long Term Prognosis.- 6. Case histories. -7. Fifty years of Landau-Kleffner Syndrome. Part II. Related Central Auditory Disorders.- 8. Adrenoleukodystrophy.- 9. Cerebrovascular accidents.- 10. Auditory agnosia in children after Herpes Encephalitis.- 11. Transient auditory agnosia /cortical deafness during the recovery phase of acute encephalopathy of unknown origin. -12. Pelizaeus-Merzbacher Disease. -13. Long-term hydrocephalus. -14. Brain malformation and hydrocephalus